Multiple Ecchordosis Physaliphora: A Challenging Diagnosis
نویسندگان
چکیده
Ecchordosis physaliphora (EP) is a benign congenital hamartoma of the ectopic notochordal remnant, accounting for 0.5–2% of all autopsies, and found in 1.5% of all magnetic resonance imaging (MRI) of the brain. It commonly occurs along the midline within the retroclival and the prepontine cistern. EP has a slow growth rate and can vary in size from a few mm to 2 cm.[1] Giant symptomatic EPs are extremely rare, and only four cases have been reported in the literature.[2‐5] No cases of multiple EPs or EPs with metastasis have been reported.
منابع مشابه
A case of ecchordosis physaliphora presenting with an intratumoral hemorrhage.
Ecchordosis physaliphora is a rare congenital, benign, hamartomatous, retroclival mass derived from notochordal tissue that is typically located intradurally in the prepontine cistern. Ecchordosis physaliphora is usually asymptomatic. In rare cases, ecchordosis physaliphora can be symptomatic due to tumor expansion and compression of the surrounding structures and extratumoral hemorrhage. To ou...
متن کاملProposed Diagnostic Criteria, Classification Schema, and Review of Literature of Notochord-Derived Ecchordosis Physaliphora.
Ecchordosis physaliphora (EP) is a benign notochordal remnant derived from ectopic nests found along the craniospinal axis. It typically presents asymptomatically and is diagnosed using classic radiologic features, particularly location, T1-hypointensity, T2-hyperintensity, and lack of enhancement following gadolinium (Gd) contrast administration. Distinguishing EP from its malignant counterpar...
متن کاملNotochord Pathology in the cranio-cervical junction: chordomas. Ecchordosis Physaliphora vs chordomas with low radiological agressivity: a diagnostic challenge
متن کامل
A Unique Case Of Ecchordosis Physaliphora With Intratumoral Haemorrhage
Ecchordosis physaliphora is a small, gelatinous tissue that is considered an ectopic notochordal remnant. This tissue is located in the midline of the craniospinal axis, reaching from the dorsum sellae to the sacrococcygeal region (1-4). Intracranial EP is typically found intradurally in the pre-pontine cistern, where it is attached to the dorsal wall of clivus via a small pedicle (1, 2, 5). Ec...
متن کاملTransclival Pseudomeningocele Secondary to Ecchordosis Physaliphora: Case Report and Literature Review
We describe a 52-year-old woman who presented with meningitis secondary to a pseudomeningocele within the sphenoid sinus derived from a bony defect in the clivus. The bony defect was radiologically characteristic of an ecchordosis physaliphora (EP). She underwent surgical repair of the defect and had resolution of her symptoms. This case report will discuss the second case of transclival pseudo...
متن کامل